Rare metabolic diseases and nursing care in nutritional management. Systematic review [Enfermedades raras del metabolismo y el cuidado de enfermería en la gestión nutricional. Revisión sistemática]
DOI:
https://doi.org/10.62574/7wshbb53Keywords:
nursing care, palliative care, obesity managementAbstract
to describe rare metabolic diseases and nursing care in nutritional management. Method: Systematic review of 16 scientific articles. Results and conclusion: From the results obtained, we can conclude that nutritional management is a fundamental pillar in the treatment of numerous IMDs, requiring personalised interventions according to the specific type of metabolic disorder. Likewise, nursing staff play a crucial role in the implementation and monitoring of dietary regimens, as well as in the education of patients and their families.
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